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여러 분류법이 있으나 면역표현형과 세포계열에 따른 WHO분류법을 최근에 사용하고 있습니다.
림프종의 WHO 분류 (1990년대)
B-CELL NEOPLASMS B세포신생물
Precursor B-cell neoplasm 전구B세포종양
Precursor B-lymphoblastic leukemia/lymphoma 전구B림프모세포백혈병/림프종
Precursor B-cell acute lymphoblastic leukemia 전구B급성림프모세포백혈병
Mature (peripheral) B-cell neoplasms 말초B세포종양
B-cell chronic lymphocytic leukemia/small lymphocytic lymphoma
B세포만성림프구성백혈병/소림프구성림프종B-cell prolymphocytic leukemia B세포전림프구성백혈병
Lymphoplasmacytic lymphoma 림프형질세포림프종
Splenic marginal zone B-cell lymphoma (with/without villous lymphocytes)
비장변연B세포림프종Hairy cell leukemia 모발성세포백혈병
Plasma cell myeloma/plasmacytoma 형질세포종
Extranodal marginal zone B-cell lymphoma of MALT type 림프절외변연B세포림프종
Nodal marginal zone B-cell lymphoma (with/without monocytoid B cells)
림프절변연B세포림프종Follicular lymphoma 여포성림프종
Mantle-cell lymphoma 맨틀세포림프종
Diffuse large B-cell lymphoma 미만성거대B세포림프종
Mediastinal large B-cell lymphoma 종격동거대B세포림프종
Primary effusion lymphoma 원발성삼출성림프종
Burkitt lymphoma/Burkitt cell leukemia 버킷림프종/버킷세포백혈병
T-CELL AND NK-CELL NEOPLASMS T세포와 NK세포 신생물
Precursor T-cell neoplasm 전구T세포종양
Precursor T-lymphoblastic lymphoma/leukemia 전구T림프모세포림프종
Precursor T-cell acute lymphoblastic leukemia 전구T세포급성림프모세포림프종
Mature (peripheral) T-cell neoplasms 말초T세포림프종
T-cell prolymphocytic leukemia T세포전림프구성백혈병
T-cell granular lymphocytic leukemia T세포거대과립림프구성백혈병
Aggressive NK-cell leukemia 공격성NK세포백혈병
Adult T-cell lymphoma/leukemia (HTLV-1 positive) 성인T세포백혈병/림프종
Extranodal NK/T-cell lymphoma, nasal type 림프절외NK/T세포림프종,비형태
Enteropathy-type T-cell lymphoma 장병변T세포림프종
Hepatosplenic gamma-delta T-cell lymphoma 간비감마델타T세포림프종
Subcutaneous panniculitis-like T-cell lymphoma 피하지방층양T세포림프종
Mycosis fungoides/Sezarysyndrome 균상식육종/세자리증후군
Anaplastic large-cell lymphoma, T/null cell, primary cutaneous type
역형성대세포림프종, T/null세포형, 원발피부성타입
Peripheral T-cell lymphoma, not otherwise characterized
말초T세포림프종, 미분류형
Angioimmunoblastic T-cell lymphoma 혈관면역모세포형T세포림프종
Anaplastic large-cell lymphoma, T/null cell, primary systemic type
역형성대세포림프종, T/null세포형, 원발조직타입
HODGKIN LYMPHOMA (HODGKIN DISEASE) 호지킨림프종
Nodular lymphocyte-predominant Hodgkin lymphoma 결절성림프구우세형호지킨병
Classical Hodgkin lymphoma 전형적호지킨병
Nodular sclerosis Hodgkin lymphoma (grades 1 and 2) 결절성경화형호지킨병
Lymphocyte-rich classical Hodgkin lymphoma 림프구충만성전형적호지킨병
Mixed cellularity Hodgkin lymphoma 혼합세포형호지킨병
Lymphocyte depletion Hodgkin lymphoma 림프구결핍성호지킨병